Haplotypes

Ban/Ban

(n = 35)

Ban/Ben

(n = 22)

Ben/Ben

(n = 7)

Others

(n = 11)

P

Pain rate*—n (%)

≤1 (moderate)

9 (25.7)

10 (45.5)

2 (28.6)

4 (36.4)

≥2 (severe)

26 (74.3)

12 (54.5)

5 (71.4)

7 (63.6)

0.478

HbF level—n (%)

≤2 g/dL

3 (9.7)

3 (15.8)

1 (14.3)

3 (27.3)

>2 g/dL

28 (90.3)

16 (84.2)

6 (85.7)

8 (72.7)

0.566

CE—n (%)

Yes

13 (37.1)

10 (45.5)

4 (57.1)

6 (54.5)

No

22 (62.9)

12 (54.5)

3 (42.9)

5 (45.5)

0.643